Lungs

Marfan syndrome can affect the lungs, however not everyone has issues with their lungs that has the disorder.

Pulmonary symptoms are often not a major feature of Marfan syndrome, but spontaneous pneumothorax is common. In spontaneous unilateral pneumothorax, air escapes from a lung and occupies the pleural space between the chest wall and the lung. In such cases, the lung becomes partially compressed or collapsed. As a result, this can cause pain, shortness of breath, cyanosis, and if not treated, it can cause death.

Also other pulmonary manifestations of Marfan syndrome may include sleep apnea and idiopathic obstructive lung disease.

Pathological changes in the lungs have been described such as cystic changes, emphysema, pneumonia, bronchiectasis, bullae, apical fibrosis and congenital malformations such as middle lobe hypoplasia.

It is recommended that a person with Marfan syndrome should not smoke, as it can damage the lungs even more.

Also should a person develop issues while sleeping, such as with their breathing it is advised to see your doctor, regarding this issue.

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